ICD-11-MMS
ICD-11-MMS ICD11分類(ICD-11-MMS) > CHAPTER11 循環器系の疾患(Diseases of the circulatory system) > BlockL1-BC4 心筋又は心室の疾患(Diseases of the myocardium or cardiac chambers) > BC43 心筋症(Cardiomyopathy) > BC43.0 拡張型心筋症(Dilated cardiomyopathy) > BC43.00 家族性遺伝的拡張型心筋症(Familial-genetic dilated cardiomyopathy)
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BC43.00 家族性遺伝的拡張型心筋症(Familial-genetic dilated cardiomyopathy)
分類ID 分類名 ICD11
1 10165330 家族性遺伝性拡張型心筋症(Familial-genetic dilated cardiomyopathy) BC43.00
2 20035732 家族性拡張型心筋症(familial dilated cardiomyopathy) BC43.00
3 20035733 原発性家族性拡張型心筋症(primary familial dilated cardiomyopathy) BC43.00
4 20035734 家族性うっ血型心筋症(familial congestive cardiomyopathy) BC43.00
5 20035735 家族性孤発性拡張型心筋症(Familial isolated dilated cardiomyopathy) BC43.00
6 20035736 脂肪酸酸化障害による拡張型心筋症(Dilated cardiomyopathy due to fatty acid oxidation disorder) BC43.00
7 20035737 拡張型心筋症を伴う脂肪酸酸化又はケトン生成障害(Fatty acid oxidation or ketogenesis disorder with dilated cardiomyopathy) BC43.00
8 20035738 原発性カルニチン欠乏症による拡張型心筋症(Dilated cardiomyopathy due to primary carnitine deficiency) BC43.00
9 20035739 原発性カルニチン欠乏症による拡張型低運動性心筋症(Dilated-hypokinetic cardiomyopathy due to primary carnitine deficiency) BC43.00
10 20035740 マロニル-CoA脱炭酸酵素欠損症による拡張型心筋症(Dilated cardiomyopathy due to malonyl-CoA decarboxylase deficiency) BC43.00
11 20035741 マロン酸尿による拡張型心筋症(dilated cardiomyopathy due to malonic aciduria) BC43.00
12 20035742 マロニルCoA脱炭酸酵素欠損症による拡張型低運動性心筋症(Dilated-hypokinetic cardiomyopathy due to malonyl-CoA decarboxylase deficiency) BC43.00
13 20035743 ミトコンドリアミオパチーによる拡張型心筋症(Dilated cardiomyopathy due to mitochondrial myopathy) BC43.00
14 20035744 拡張型心筋症を伴うミトコンドリア病(mitochondrial disease with dilated cardiomyopathy) BC43.00
15 20035745 ミトコンドリア拡張型心筋症(Mitochondrial dilated cardiomyopathy) BC43.00
16 20035746 組織球様心筋症(Histiocytoid cardiomyopathy) BC43.00
17 20035747 限局性脂質心筋症(focal lipid cardiomyopathy) BC43.00
18 20035748 幼児黄色腫心筋症(infantile xanthomatous cardiomyopathy) BC43.00
19 20035749 オンコサイト性心筋症(oncocytic cardiomyopathy) BC43.00
20 20035750 シトクロムCオキシダーゼ欠損症による拡張型心筋症(Dilated cardiomyopathy due to Cytochrome C oxidase deficiency) BC43.00
21 20035751 バース症候群による拡張型心筋症(Dilated cardiomyopathy due to Barth syndrome) BC43.00
22 20035752 カーンズ・セイヤー症候群による拡張型心筋症(Dilated cardiomyopathy due to Kearns–Sayre syndrome) BC43.00
23 20035753 ミトコンドリア筋症・脳症・乳酸アシドーシス・卒中様症状群による拡張型心筋症(Dilated cardiomyopathy due to MELAS) BC43.00
24 20035754 ミトコンドリア筋症・脳症・乳酸アシドーシス・卒中様症状群による拡張型心筋症(Dilated cardiomyopathy due to MELAS - [Mitochondrial Encephalopathy, Lactic acidosis and Stroke-like episodes]) BC43.00
25 20035755 赤色ぼろ線維を伴うミオクローヌスてんかんによる拡張型心筋症(Dilated cardiomyopathy due to MERRF) BC43.00
26 20035756 MERRF[赤色ぼろ線維を伴うミオクローヌスてんかん]による拡張型心筋症(Dilated cardiomyopathy due to MERRF - [myoclonic epilepsy with ragged-red fibers]) BC43.00
27 20035757 神経筋疾患による拡張型心筋症(Dilated cardiomyopathy due to neuromuscular disease) BC43.00
28 20035758 拡張型心筋症を伴う神経筋疾患(Neuromuscular disease with dilated cardiomyopathy) BC43.00
29 20035759 ジストロフィン症による拡張型心筋症(Dilated cardiomyopathy due to dystrophinopathy) BC43.00
30 20035760 デュシェンヌ型筋ジストロフィによる拡張型心筋症(Dilated cardiomyopathy due to Duchenne muscular dystrophy) BC43.00
31 20035761 ベッカー型筋ジストロフィによる拡張型心筋症(Dilated cardiomyopathy due to Becker muscular dystrophy) BC43.00
32 20035762 ラミノパチーによる拡張型心筋症(Dilated cardiomyopathy due to laminopathy) BC43.00
33 20035763 ラミノパチー[LMNA]による拡張型心筋症(Dilated cardiomyopathy due to laminopathy [LMNA]) BC43.00
34 20035764 ラミンA/C変異による拡張型心筋症(Dilated cardiomyopathy due to lamin A/C mutation) BC43.00
35 20035765 LMNA変異による刺激伝導障害を伴う家族性拡張型心筋症(Familial dilated cardiomyopathy with conduction defect due to LMNA mutation) BC43.00
36 20035766 エメリー・ドライフス型筋ジストロフィによる拡張型心筋症(Dilated cardiomyopathy due to Emery-Dreifus muscular dystrophy) BC43.00
37 20035767 肢帯型ジストロフィによる拡張型心筋症(Dilated cardiomyopathy due to limb-girdle muscular dystrophy) BC43.00
38 20035768 先天性筋ジストロフィによる拡張型心筋症(Dilated cardiomyopathy due to congenital muscular dystrophy) BC43.00
39 20035769 脊髄性筋委縮症による拡張型心筋症(Dilated cardiomyopathy due to spinal muscular atrophy) BC43.00
40 20035770 SMA[脊髄性筋萎縮症]による拡張型心筋症(Dilated cardiomyopathy due to SMA - [spinal muscular atrophy]) BC43.00
41 20035771 多発筋炎による拡張型心筋症(Dilated cardiomyopathy due to polymyositis) BC43.00
42 20035772 サルコメア拡張型心筋症(Sarcomeric dilated cardiomyopathy) BC43.00
43 20035773 X染色体関連乳幼児拡張型心筋症(X-linked infantile dilated cardiomyopathy) BC43.00
44 20035774 ライソゾーム病による拡張型心筋症(Dilated cardiomyopathy due to lysosomal storage disorder) BC43.00
45 20035775 ライソゾーム病による拡張型低運動性心筋症(dilated-hypokinetic cardiomyopathy due to lysosomal storage disorder) BC43.00
46 20035776 ムコ多糖症による拡張型心筋症(Dilated cardiomyopathy due to mucopolysaccharidoses) BC43.00
47 20035777 ムコ多糖症による拡張型低運動性心筋症(dilated-hypokinetic cardiomyopathy due to mucopolysaccharidoses) BC43.00
48 20035778 スフィンゴ脂質蓄積症による拡張型心筋症(Dilated cardiomyopathy due to sphingolipidoses) BC43.00
49 20035779 スフィンゴ脂質蓄積症による拡張型低運動性心筋症(dilated-hypokinetic cardiomyopathy due to sphingolipidoses) BC43.00
50 20035780 ゴーシェ病による拡張型心筋症(Dilated cardiomyopathy due to Gaucher disease) BC43.00